Abstract
Double-chambered right ventricle (DCRV) caused by right ventricular outflow tract
obstruction, is a developmental cardiac anomaly in which the anomalous muscle bundles
divide the right ventricular cavity into two chambers. Few cases with DCRV coexisting
with severe aortic stenosis (AS) have been reported. Moreover, adult cases are extremely
uncommon.
We report an elderly case of a heavy DCRV with severe AS detected by transthoracic
echocardiography and catheterization study. An 85-year-old woman with dyspnea on effort
and right-sided heart failure was diagnosed with DCRV and severe AS by echocardiography.
She underwent a resection of the anomalous muscle of the right ventricle and aortic
valve replacement. Her symptoms disappeared postoperatively and was discharged home.
At 2 years postoperatively, she was generally well without recurrence of DCRV. In
conclusion, the case of DCRV with AS is rare and surgery is useful to relieve the
heart failure symptoms and improve the prognosis of both young and adult patients.
Learning objective
Double-chambered right ventricle (DCRV) is uncommon in the older population; however,
clinicians should consider DCRV in patients with right-sided heart failure as a differential
diagnosis. The case of DCRV with aortic stenosis is rare, surgical treatment is particularly
useful for these patients to relieve the heart failure symptoms and improve the prognosis
in young and adult cases.
Keywords
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Article info
Publication history
Published online: January 10, 2023
Accepted:
December 5,
2022
Received in revised form:
November 28,
2022
Received:
July 24,
2022
Publication stage
In Press Corrected ProofIdentification
Copyright
© 2023 Japanese College of Cardiology. Published by Elsevier Ltd. All rights reserved.
