Abstract
Herein, we present a rare case of papillary fibroelastoma of the aortic valve, which
caused severe aortic stenosis. The papillary fibroelastoma developed on the left ventricular
side of the non-coronary cusp, immobilizing the cusp motion and obstructing the left
ventricular outflow tract, resulting in severe aortic stenosis that brought on acute
heart failure. The patient underwent an urgent surgical treatment, which resulted
in a successful outcome. To the best of our knowledge, this is the first case of papillary
fibroelastoma in which aortic stenosis was so severe as to cause congestive heart
failure.
Learning objective
Papillary fibroelastoma (PFE) is the most commonly observed primary cardiac tumor
in adults that commonly involves left heart chambers. While PFEs often cause embolisms,
they rarely cause valvular dysfunction. In a case presented herein, a PFE developed
on the left ventricular side of the non-coronary cusp, immobilizing the cusp motion
and obstructing the left ventricular outflow tract, resulting in severe aortic stenosis
that brought on acute heart failure.
Keywords
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Article info
Publication history
Published online: December 17, 2022
Accepted:
November 14,
2022
Received in revised form:
October 25,
2022
Received:
June 18,
2022
Identification
Copyright
© 2022 Japanese College of Cardiology. Published by Elsevier Ltd. All rights reserved.
