Herein, we present a rare case of papillary fibroelastoma of the aortic valve, which caused severe aortic stenosis. The papillary fibroelastoma developed on the left ventricular side of the non-coronary cusp, immobilizing the cusp motion and obstructing the left ventricular outflow tract, resulting in severe aortic stenosis that brought on acute heart failure. The patient underwent an urgent surgical treatment, which resulted in a successful outcome. To the best of our knowledge, this is the first case of papillary fibroelastoma in which aortic stenosis was so severe as to cause congestive heart failure.
Papillary fibroelastoma (PFE) is the most commonly observed primary cardiac tumor in adults that commonly involves left heart chambers. While PFEs often cause embolisms, they rarely cause valvular dysfunction. In a case presented herein, a PFE developed on the left ventricular side of the non-coronary cusp, immobilizing the cusp motion and obstructing the left ventricular outflow tract, resulting in severe aortic stenosis that brought on acute heart failure.
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- Prognostic and bioepidemiologic implications of papillary fibroelastomas.J Am Coll Cardiol. 2015; 65: 2420-2429
- Cardiac papillary fibroelastoma: a comprehensive analysis of 725 cases.Am Heart J. 2003; 146: 404-410
- Clinical and echocardiographic characteristics of papillary fibroelastomas: a retrospective and prospective study in 162 patients.Circulation. 2001; 103: 2687-2693
- Surgical treatment of cardiac papillary fibroelastoma: a single center experience with eighty-eight patients.Ann Thorac Surg. 2005; 80: 1712-1718
- Papillary fibroelastoma of the aortic valve: analysis of 21 cases, including a presentation with cardiac arrest.Tex Heart Inst J. 2015; 42: 131-135
- Aortic valve papillary fibroelastoma associated with severe aortic regurgitation: a comprehensive assessment with 2- and 3-dimensional transesophageal echocardiography.J Am Coll Cardiol. 2012; 60e41
- Surgical experience with cardiac papillary fibroelastoma over a 15-year period.Ann Thorac Surg. 2012; 94: 537-541
- The characteristics and outcomes of native aortic valve thrombosis: a systematic review.J Am Coll Cardiol. 2021; 78: 811-824
- Cardiac calcified amorphous tumor: a systematic review of the literature.Int J Cardiol Heart Vasc. 2015; 7: 1-5
- Giant multiple Lambl's excrescences mimicking vegetation.Asian Cardiovasc Thorac Ann. 2022; 30: 864-865
Published online: December 17, 2022
Accepted: November 14, 2022
Received in revised form: October 25, 2022
Received: June 18, 2022
© 2022 Japanese College of Cardiology. Published by Elsevier Ltd. All rights reserved.