An undifferentiated, pleomorphic cardiac sarcoma masquerading as myxoma

Published:October 10, 2022DOI:


      Cardiac sarcoma is a very rare cause of primary cardiac tumor. We present a case of an undifferentiated, pleomorphic cardiac sarcoma, masquerading as a cardiac myxoma on multimodal imaging evaluation, which was definitively diagnosed on intra-operative histopathologic examination followed by surgical resection.

      Learning objective

      Evaluate and diagnose a rare primary cardiac tumor via multimodal imaging and a multidisciplinary approach.


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